What is a DKS anastomosis?

The Damus-Kaye-Stansel anastomosis was originally described for the treatment of transposition of the great arteries but it is now used mainly for the treatment of single ventricle anomalies in patients who are at risk of developing systemic ventricular outflow tract obstruction.

What is the purpose of the Fontan procedure?

Introduction. The Fontan procedure refers to any surgical procedure that leads to systemic flow of venous blood to the lungs without passing through a ventricle. In 1971, Fontan and Baudet (1) described a surgical procedure for repair of tricuspid atresia that built on experimental and clinical research from the 1940s.

What is the first surgical repair for a hypoplastic left heart?

The Norwood procedure is a type of open-heart surgery for babies born with hypoplastic left heart syndrome. It is usually done in the first few weeks of life.

How long does a Fontan procedure take?

How long does the Fontan procedure take? This surgical procedure usually takes about four hours to perform. There are not as many risks following this surgery as are seen with the Norwood procedure. The amount of time your child will need to be in the hospital is usually around 10 to 14 days.

Is DKS part of Norwood?

The Damus–Kaye–Stansel (DKS) operation is a palliative procedure for patients with a single functioning ventricle with an obstructed rudimentary outflow chamber. It is not used for treatment of hypoplastic left heart syndrome which is treated using the Norwood procedure.

How does a BT shunt work?

A BT shunt is tiny, measuring less than 5 millimeters (0.20 inches) in diameter. A surgeon attaches the two ends of the shunt to a major blood vessel, such as the subclavian artery, and to the pulmonary artery. The high-pressure arterial system will force blood through the BT shunt to the lungs to pick up more oxygen.

How risky is Fontan procedure?

In research published in Journal of the American College of Cardiology in 2016, Dr. Egbe and colleagues studied 278 adult patients with atrial arrhythmias who underwent Fontan procedures and estimated a thromboembolic complication rate of 6.5 per 100 patient-years.

What are the 3 surgeries for hypoplastic left heart syndrome?

The series of three reconstructive operations to repair HLHS — the Norwood, Glenn and Fontan procedures — is known as ” Staged Reconstruction .” Frequent surveillance in infancy and early childhood is important to minimize risk factors for the eventual Fontan operation.

How old is the oldest HLHS Survivor?

The oldest living person with HLHS is their 30s. Ultimately, the Cribbs hope and pray that Leigh Ann has a long life ahead of her.

What age is Fontan for?

The Fontan procedure is a type of open-heart surgery. Children who need this surgery usually have it when they’re 18–36 months old.

What is DKS in cardiology?

The Damus–Kaye–Stansel (DKS) procedure is a cardiovascular surgical procedure used as part of the repair of some congenital heart defects. This procedure joins the pulmonary artery and the aorta in situations where the systemic circulation is obstructed.

What is the Glenn procedure in cardiac surgery?

During the Glenn procedure, the surgeon disconnects the superior vena cava (SVC) from the heart and connects it to the pulmonary artery. Now the blood from the upper part of the body flows directly into the pulmonary artery. The pulmonary artery takes the blood to the lungs.

How long does a BT shunt last?

The BT shunt mimics the role of the ductus arteriosus. It is often put in place after the ductus closes naturally. Shunts are usually used for four to five months, until the child outgrows them and a second operation or definitive repair is needed.

When is a BT shunt performed?

Postsurgical Cardiac Conditions and Transplantation The Blalock-Taussig (B-T) shunt is one of the most common pulmonary-to-systemic shunt procedures performed in children with cyanotic heart disease as a palliative therapy before a definitive correction is performed.

What was the survival rate of a Fontan procedure?

Fontan type was atriopulmonary (AP) connection in 201 and total cavopulmonary connection (TCPC) in 482 patients. Of the TCPCs, 249 were lateral tunnels and 233 were extracardiac conduits. Survival for the entire cohort was 90% at 30 years and 80% at 40 years of life.

What is the life expectancy of a child with HLHS?

Most infants die within the first two weeks of life, with an average age at death of 4.5 days (31,33,34). Some patients with HLHS, however, can survive beyond sixty days, without any surgical intervention through the development of pulmonary hypertension (8,33).

What is the life expectancy of someone with HLHS?

What are the chances of having another baby with HLHS?

Individuals who have a personal or family history of CHD have a higher chance of a heart defect happening again in the family. For most people, the risk of having another child with a congenital heart defect ranges from 3-5 percent. However, for those who have particularly rare conditions, the risk can go up to 50%.

What is the original DKS procedure?

The original DKS procedure was an end-to-side anastomosis between the main pulmonary artery and the ascending aorta. Since then, there have been numerous articles proposing modified DKS procedures.

How effective is the DKS procedure to minimize the risk of svoto?

In conclusion, the DKS procedure is an effective way to minimize the risk of SVOTO, and there are few differences in the outcomes of the DKS procedure according to the surgical technique used. Footnotes

What are the possible modifications of the DKS procedure for aortic dissection?

Later modifications of the DKS procedure include surgical closure of the aortic valve to prevent development of aortic valve insufficiency [ 2, 3] and patch augmentation of the aortic arch if the arch is hypoplastic. Figures 27.1, 27.2, 27.3, and 27.4 demonstrate the DKS procedure.

What happened to the patient who had coarctoplasty before DKS?

This patient underwent PAB, coarctoplasty, and infracardiac obstructive total anomalous pulmonary venous connection repair before the DKS procedure. He was discharged on postoperative day 10 without any problems after the DKS with BCPS operation. However, 7 months later, he was admitted via the emergency room owing to general weakness.